Anti-CLN3 antibody
| 英文名称 | CLN3 |
| 中文名称 | 神经细胞蜡样质脂褐质沉积病蛋白CLN3抗体 |
| 别 名 | Batten disease protein; Battenin; BTS; Ceroid lipofuscinosis neuronal 3; Ceroid lipofuscinosis neuronal 3 juvenile (Batten Spielmeyer Vogt disease); Ceroid lipofuscinosis neuronal 3 juvenile; CLN 3; MGC102840; Protein CLN3; CLN3_HUMAN. |
DATASHEET
Host:Rabbit
Target Protein:CLN3
IR:Immunogen Range:75-140/438
Clonality:Polyclonal
Isotype:IgG
Entrez Gene:1201
Swiss Prot:Q13286
Source:KLH conjugated synthetic peptide derived from human CLN3:75-140/438
Purification:affinity purified by Protein A
Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
Background:This gene encodes a protein that is involved in lysosomal function. Mutations in this, as well as other neuronal ceroid-lipofuscinosis (CLN) genes, cause neurodegenerative diseases commonly known as Batten disease or collectively known as neuronal ceroid lipofuscinoses (NCLs). Many alternatively spliced transcript variants have been found for this gene.
Size:100ul
Concentration:1mg/ml
Applications:WB(1:500-2000)
ELISA(1:5000-10000)
Cross Reactive Species:Human
Mouse
Rat
Cow
Horse
Rabbit
Monkey
macaque.
For research use only. Not intended for diagnostic or therapeutic use.
VALIDATION IMAGES
Sample: Bone (Mouse) Lysate at 40 ug
Primary: Anti-CLN3 (bs-8016R) at 1/300 dilution
Secondary: IRDye800CW Goat Anti-Rabbit IgG at 1/20000 dilution
Predicted band size: 48 kD
Observed band size: 50 kD
Sample:
Heart (Mouse) Lysate at 40 ug
Primary: Anti- CLN3 (bs-8016R) at 1/1000 dilution
Secondary: IRDye800CW Goat Anti-Rabbit IgG at 1/20000 dilution
Predicted band size: 48 kD
Observed band size: 50 kD
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