Anti-MMAA/cblA antibody
| 英文名称 | MMAA/cblA |
| 中文名称 | 甲基丙二酸尿症cblA抗体 |
| 别 名 | mitochondrial; cblA; MMAA protein; Methylmalonic aciduria (cobalamin deficiency) cblA type; Methylmalonic aciduria (cobalamin deficiency) type A; Methylmalonic aciduria type A protein; Methylmalonic aciduria type A protein mitochondrial; MMAA; MMAA_HUMAN. |
DATASHEET
Host:Rabbit
Target Protein:MMAA/cblA
IR:Immunogen Range:21-120/418
Clonality:Polyclonal
Isotype:IgG
Entrez Gene:166785
Swiss Prot:Q8IVH4
Source:KLH conjugated synthetic peptide derived from human MMAA/cblA:21-120/418
Purification:affinity purified by Protein A
Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
Background:The protein encoded by this gene is involved in the translocation of cobalamin into the mitochondrion, where it is used in the final steps of adenosylcobalamin synthesis. Adenosylcobalamin is a coenzyme required for the activity of methylmalonyl-CoA mutase. Defects in this gene are a cause of methylmalonic aciduria. [provided by RefSeq, Jul 2008].
Size:100ul
Concentration:1mg/ml
Applications:WB(1:500-2000)
ELISA(1:5000-10000)
Cross Reactive Species:Human
Mouse
Rat
.
For research use only. Not intended for diagnostic or therapeutic use.
VALIDATION IMAGES
Sample:
Stomach (Mouse) Lysate at 40 ug
Primary: Anti- MMAA'cblA (bs-9961R) at 1/1000 dilution
Secondary: IRDye800CW Goat Anti-Rabbit IgG at 1/20000 dilution
Predicted band size: 39 kD
Observed band size: 39 kD
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