Anti-OTC/Ornithine Carbamoyltransferase antibody (bs-18037R)

Anti-OTC/Ornithine Carbamoyltransferase antibody

DATASHEET

Host:Rabbit

Target Protein:OTC/Ornithine Carbamoyltransferase

IR:Immunogen Range:31-130/354

Clonality:Polyclonal

Isotype:IgG

Entrez Gene:5009

Swiss Prot:P00480

Source:KLH conjugated synthetic peptide derived from human OTC/Ornithine Carbamoyltransferase:31-130/354 

Purification:affinity purified by Protein A

Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.

Background:This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008]

Size:100ul

Concentration:1mg/ml

Applications:WB(1:500-2000)
ELISA(1:5000-10000)

Cross Reactive Species:Human
Mouse
Rat
Dog
Pig
Cow
Horse
Sheep
.

For research use only. Not intended for diagnostic or therapeutic use.

VALIDATION IMAGES

Sample:
Liver (Mouse) Lysate at 40 ug
Liver (Rat) Lysate at 40 ug
Primary: Anti- OTC/Ornithine Carbamoyltransferase (bs-18037R) at 1/300 dilution
Secondary: IRDye800CW Goat Anti-Rabbit IgG at 1/20000 dilution
Predicted band size: 36 kD
Observed band size: 36 kD