Anti-IDUA antibody
| 英文名称 | IDUA |
| 中文名称 | 己醛醣酸盐水解酵素抗体 |
| 别 名 | Alpha L iduronidase; IDA; Iduronidase alpha L; MPS1. |
DATASHEET
Host:Rabbit
Target Protein:IDUA
IR:Immunogen Range:561-653/653
Clonality:Polyclonal
Isotype:IgG
Entrez Gene:3425
Swiss Prot:P35475
Source:KLH conjugated synthetic peptide derived from human IDUA:561-653/653
Purification:affinity purified by Protein A
Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
Background:This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008]
Size:100ul
Concentration:1mg/ml
Applications:ELISA(1:5000-10000)
IHC-P(1:100-500)
IHC-F(1:100-500)
ICC(1:100-500)
IF(1:100-500)
Cross Reactive Species:Human
Mouse
.
For research use only. Not intended for diagnostic or therapeutic use.
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