Anti-MCEE antibody
英文名称 | MCEE |
中文名称 | MCEE蛋白抗体 |
别 名 | DL methylmalonyl CoA racemase; DL-methylmalonyl-CoA racemase; EC 5.1.99.1; GLOD2; Glyoxalase domain containing 2; MCEE; MCEE_HUMAN; Methylmalonyl CoA epimerase; Methylmalonyl-CoA epimerase; methylmalonyl-CoA epimerase, mitochondrial; mitochondrial; OTTHUMP00000160122. |
DATASHEET
Host:Rabbit
Target Protein:MCEE
IR:Immunogen Range:101-176/176
Clonality:Polyclonal
Isotype:IgG
Entrez Gene:84693
Swiss Prot:Q96PE7
Source:KLH conjugated synthetic peptide derived from human MCEE:101-176/176
Purification:affinity purified by Protein A
Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
Background:MCEE is a 176 amino acid mitochondrial protein that belongs to the glyoxalase I family. MCEE catalyzes the interconversion of D- and L-methylmalonyl-CoA during the breakdown of branched chain amino acids. The gene encoding MCEE maps to human chromosome 2p13.3. Defects in the MCEE gene are the cause of an autosomal recessive disease known as methylmalonyl-CoA epimerase deficiency (MCEE deficiency), methylmalonyl-CoA racemase deficiency or methylmalonic aciduria type 3, which is characterized by mild to moderate methylmalonic aciduria.
Size:100ul
Concentration:1mg/ml
Applications:ELISA(1:5000-10000)
IHC-P(1:100-500)
IHC-F(1:100-500)
ICC(1:100-500)
IF(1:100-500)
Cross Reactive Species:Human
Mouse
Rat
Chicken
Dog
Horse
.
For research use only. Not intended for diagnostic or therapeutic use.
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